ICD-10-CM Diagnosis Code D81.819
Diagnosis Code: D81.819 (Raw: D81819)
Description: Biotin-dependent carboxylase deficiency, unspecified
Classification: International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM)
Fiscal Year: 2026
CMS Section 111 Status: Valid for reporting.
Overview & Clinical Details
ICD-10-CM code D81.819 is designated for Biotin-dependent carboxylase deficiency, unspecified. In medical documentation and insurance billing, this code is utilized to specify medical diagnosis for patient records, reimbursement workflows, and compliance under CMS Section 111 mandatory insurer reporting guidelines.
