ICD-10-CM Diagnosis Code E71.110
Diagnosis Code: E71.110 (Raw: E71110)
Description: Isovaleric acidemia
Classification: International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM)
Fiscal Year: 2026
CMS Section 111 Status: Valid for reporting.
Overview & Clinical Details
ICD-10-CM code E71.110 is designated for Isovaleric acidemia. In medical documentation and insurance billing, this code is utilized to specify medical diagnosis for patient records, reimbursement workflows, and compliance under CMS Section 111 mandatory insurer reporting guidelines.
