ICD-10-CM Diagnosis Code E71.541
Diagnosis Code: E71.541 (Raw: E71541)
Description: Zellweger-like syndrome
Classification: International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM)
Fiscal Year: 2026
CMS Section 111 Status: Valid for reporting.
Overview & Clinical Details
ICD-10-CM code E71.541 is designated for Zellweger-like syndrome. In medical documentation and insurance billing, this code is utilized to specify medical diagnosis for patient records, reimbursement workflows, and compliance under CMS Section 111 mandatory insurer reporting guidelines.
