ICD-10 Code E78.010 - Homozygous familial hypercholesterolemia [HoFH]

ICD-10-CM Diagnosis Code E78.010

Diagnosis Code: E78.010 (Raw: E78010)

Description: Homozygous familial hypercholesterolemia [HoFH]

Classification: International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM)

Fiscal Year: 2026

CMS Section 111 Status: Valid for reporting (Excluded from No-Fault liability reporting).

Overview & Clinical Details

ICD-10-CM code E78.010 is designated for Homozygous familial hypercholesterolemia [HoFH]. In medical documentation and insurance billing, this code is utilized to specify medical diagnosis for patient records, reimbursement workflows, and compliance under CMS Section 111 mandatory insurer reporting guidelines.