ICD-10-CM Diagnosis Code H49.813
Diagnosis Code: H49.813 (Raw: H49813)
Description: Kearns-Sayre syndrome, bilateral
Classification: International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM)
Fiscal Year: 2026
CMS Section 111 Status: Valid for reporting.
Overview & Clinical Details
ICD-10-CM code H49.813 is designated for Kearns-Sayre syndrome, bilateral. In medical documentation and insurance billing, this code is utilized to specify medical diagnosis for patient records, reimbursement workflows, and compliance under CMS Section 111 mandatory insurer reporting guidelines.
