ICD-10-CM Diagnosis Code D81.818
Diagnosis Code: D81.818 (Raw: D81818)
Description: Other biotin-dependent carboxylase deficiency
Classification: International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM)
Fiscal Year: 2026
CMS Section 111 Status: Valid for reporting.
Overview & Clinical Details
ICD-10-CM code D81.818 is designated for Other biotin-dependent carboxylase deficiency. In medical documentation and insurance billing, this code is utilized to specify medical diagnosis for patient records, reimbursement workflows, and compliance under CMS Section 111 mandatory insurer reporting guidelines.
