ICD-10 Code E79.81 - Aicardi-Goutieres syndrome

ICD-10-CM Diagnosis Code E79.81

Diagnosis Code: E79.81 (Raw: E7981)

Description: Aicardi-Goutieres syndrome

Classification: International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM)

Fiscal Year: 2026

CMS Section 111 Status: Valid for reporting.

Overview & Clinical Details

ICD-10-CM code E79.81 is designated for Aicardi-Goutieres syndrome. In medical documentation and insurance billing, this code is utilized to specify medical diagnosis for patient records, reimbursement workflows, and compliance under CMS Section 111 mandatory insurer reporting guidelines.